Arrhythmic Mitral Valve Prolapse: Late Correct Diagnosis Publisher



Mirshafiee S¹ ; Aamaraee Z¹ ; Eftekhari M¹ ; Mollazadeh R¹
Source: JACC: Case Reports Published:2025

Abstract

Background: Arrhythmic mitral valve prolapse (AMVP) is a relatively new entity in the field of arrhythmia and sudden cardiac death. Case Summary: A 19-year-old female patient with a history of aborted sudden cardiac death, initially diagnosed as idiopathic ventricular fibrillation in 2012 and received implantable cardioverter defibrillator. Gradual decline in left ventricular ejection fraction and receiving multiple appropriate implantable cardioverter defibrillator shocks was odd for us. After review of her past medical documents and detailed cardiac imaging diagnosis of AMVP was made. Discussion: Individuals with AMVP are prone to left ventricular mechanical dispersion, leading to an increased susceptibility to malignant ventricular arrhythmias independent of the severity of MR. Take-Home Message: This case emphasizes the importance of reviewing old documents and consultation with multiple subspecialists. Follow-up may alter the primary suspected diagnosis. © 2025 The Authors