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Orbicularis Oculi Myectomy As a Treatment for Blepharospasm in a Case of Schwartz Jampel Syndrome Publisher



Eshraghi B1 ; Shadravan M2 ; Aalami E2 ; Pour EK2
Authors

Source: Journal of Ophthalmic and Vision Research Published:2016


Abstract

Purpose: To describe a patient with Schwartz Jampel vel Aberfeld syndrome (SJS) who underwent orbicularis oculi myectomy as a treatment for blepharospasm. Case Report: A 4-year-old child with SJS did not respond to an injection of a single dose of botulinum toxin after one month, so orbicularis myectomy was then performed under general anesthesia. During the procedure, orbicularis vermiform movements were a useful guide for the extent of myectomy that the patient needed. He responded very well to this procedure and experienced significant relief of blepharospasm documented in follow-up visits for up to 6 months. Conclusion: Blepharospasm in patients with SJS can be treated with orbicularis oculi myectomy as a good functional method with faster and durable response in comparison to botulinum toxin injection. © 2016 Journal of Ophthalmic and Vision Research.